Kulak heliksinde hmb-45 negatif dev kutanöz anjiomyolipom olgu sunumu ve literatür taraması
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Dosyalar
Tarih
2021
Yazarlar
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Aksaray Üniversitesi
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Anjiomyolipom (AML), genellikle böbrekte tek veya multipl kitle olarak görülen, değişen oranlarda düz kas, yağ ve kan damar komponentleri olan bir tümördür. AML, %20 oranında tüberoskleroz (TBC) ile ilişkili olabilen böbrekte görülen en sık benign tümördür. TBC ilişkili tümörler genellikle bilateral olma eğilimindedir. Böbrek dışı AML vakaları oldukça nadirdir ve genellikle karaciğer, nasal kavite, kalp, akciğer ve deride tariflenmiştir. Kutanöz AML’ler çoğunlukla soliter, invazyon göstermeyen, TBC ilişkisi olmayan, eksizyonel olarak çıkarılması yeterli vakalardır. Bugüne kadar İngiliz literatüründe 21 kutanöz AML vakası bildirilmiştir. 50 yaşında erkek hastamızda kulak heliksinde belirgin bulgusu olmayan, uzun süredir var olan, soliter nodül şeklinde kitle kozmetik nedenlerle çıkarılan ve kutanöz AML tanısı alan vakamızı, nadir bir lokalizasyon ve büyüklüğü sebebiyle sunmak istedik.
Introduction: Angiomyolipoma (AML) is a tumor with varying proportions of smooth muscle, fat and blood vessel components, usually seen as a single or multiple mass in the kidney. AML is the most common benign tumor seen in the kidney, which may be associated with tuberous sclerosis (TSC) at a rate of 20%. Case: In our 50-year-old male patient, a long-standing solitary nodule lesion with no obvious findings in the ear helix was removed for cosmetic reasons and was diagnosed with cutaneous AML. Result: TSC-associated AML usually tends to be bilateral. Cases of extrarenal AML are extremely rare and have usually been described in the liver, nasal cavity, heart, lung, and skin. Cutaneous AMLs are mostly solitary, noninvasive, unrelated to TSC, and sufficient for excisional removal. To date, 21 cases of cutaneous AML have been reported in the English literature. We wanted to present our case because of its rare localization and size.
Introduction: Angiomyolipoma (AML) is a tumor with varying proportions of smooth muscle, fat and blood vessel components, usually seen as a single or multiple mass in the kidney. AML is the most common benign tumor seen in the kidney, which may be associated with tuberous sclerosis (TSC) at a rate of 20%. Case: In our 50-year-old male patient, a long-standing solitary nodule lesion with no obvious findings in the ear helix was removed for cosmetic reasons and was diagnosed with cutaneous AML. Result: TSC-associated AML usually tends to be bilateral. Cases of extrarenal AML are extremely rare and have usually been described in the liver, nasal cavity, heart, lung, and skin. Cutaneous AMLs are mostly solitary, noninvasive, unrelated to TSC, and sufficient for excisional removal. To date, 21 cases of cutaneous AML have been reported in the English literature. We wanted to present our case because of its rare localization and size.
Açıklama
Anahtar Kelimeler
Kutanöz Anjiomyolipom, HMB-45, Kulak Heliksi, Cutaneous Angiomyolipoma, Ear Helix
Kaynak
Aksaray Üniversitesi Tıp Bilimleri Dergisi / Aksaray University Journal of Medical Sciences
WoS Q Değeri
Scopus Q Değeri
Cilt
2
Sayı
1
